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Long-read sequencing of families reveals increased germline and postzygotic mutation rates in repetitive DNA - PubMed

3 days ago
  • #genetics
  • #sequencing
  • #mutation
  • Long-read sequencing enhances detection of mutations in repetitive DNA regions.
  • Study involved 73 children from 42 autism families, totaling 157 individuals.
  • Average of 95 de novo mutations per transmission observed.
  • No significant difference in mutation rates between affected and unaffected siblings.
  • Long-read sequencing increases de novo mutation discovery by 20-40%.
  • Germline mutation rate is 1.30×10^-8 substitutions/base pair/generation.
  • Postzygotic mutation rate is 0.23×10^-8 substitutions/base pair/generation.
  • Mutation rates are higher in repetitive DNA, influenced by length and identity.
  • Postzygotic mutations in repeats likely due to faulty DNA repair and interlocus gene conversion.