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How to monitor disease progression in ATTR amyloid cardiomyopathy: Implications for clinical practice and trial design - PubMed

11 hours ago
  • #Disease Progression
  • #ATTR-CM
  • #Cardiac Biomarkers
  • ATTR amyloid cardiomyopathy (ATTR-CM) is no longer considered a rare and fatal condition due to new therapies.
  • Monitoring disease progression is crucial for clinical decision-making and personalized treatment strategies.
  • Key indicators include worsening heart failure symptoms, diuretic use, 6-minute walk test decline, and cardiac biomarkers.
  • An integrated, multiparametric approach is recommended for precise disease assessment.
  • Novel therapies aim to clear amyloid deposits, offering potential for disease regression.
  • Future clinical trials may use disease progression criteria as surrogate endpoints.