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Recurrent aquaporin 4-immunoglobulin G-positive neuromyelitis optica spectrum disorder in a patient with long-standing rheumatoid arthritis: A case report - PubMed

17 hours ago
  • #autoimmune disorders
  • #neuromyelitis optica spectrum disorder
  • #rheumatoid arthritis
  • Aquaporin 4-IgG positive neuromyelitis optica spectrum disorder (NMOSD) is an autoimmune condition affecting optic nerves and spinal cord.
  • Co-occurrence of NMOSD and rheumatoid arthritis (RA) is rare, with only 15 cases reported globally.
  • A 34-year-old woman with long-standing RA developed relapsing NMOSD, highlighting risk of misdiagnosis as stroke in autoimmune patients with neurological symptoms.
  • The report examines shared immunopathological mechanisms and suggests integrated treatment strategies for managing both disorders.
  • It emphasizes the need for prompt brain/spinal cord MRI and aquaporin 4-IgG testing in RA patients with optic neuritis, a gap in current guidelines.