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Desmin mutations in cardiomyocytes increase susceptibility to coxsackievirus B3 infection by impairing antiviral IFN-β response and upregulating viral receptors expression - PubMed

3 hours ago
  • #cardiomyopathy
  • #genetic mutation
  • #viral infection
  • Desmin mutations in cardiomyocytes increase susceptibility to Coxsackievirus B3 (CVB3) infection.
  • Mutations impair antiviral IFN-β response and upregulate viral receptors (CAR and cell-surface vimentin).
  • Human iPSC-derived cardiomyocytes (hiPSC-CMs) with DES mutations show enhanced viral replication and reduced contractility.
  • CVB3 infection worsens structural disorganization and desmin aggregation in mutation-specific ways.
  • Study reveals a pathogenic synergy between genetic cytoskeletal defects and viral infection in cardiac dysfunction.