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Tissue characterization in cardiac amyloidosis: a joint consensus document by the gruppo di studio di cardiopatologia (SIAPEC) and the SIC/ANMCO Italian cardiac amyloidosis network (RIAC) - PubMed

4 days ago
  • #amyloid typing
  • #tissue characterization
  • #cardiac amyloidosis
  • Cardiac amyloidosis (CA) is caused by abnormal protein fibril accumulation in the myocardium.
  • Targeted therapies for light-chain amyloidosis (AL) and transthyretin amyloidosis (ATTR) require prompt diagnosis and accurate protein typing.
  • Diagnostic confirmation often requires biopsy, especially for AL and rare CA variants.
  • Amyloid typing techniques include immunohistochemistry, immunofluorescence, immune electron microscopy, and mass spectrometry.
  • The document provides guidance on tissue analysis and amyloid typing for clinical practice.