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Preserving the UFMylation-cilium axis mitigates blue light-induced retinal degeneration - PubMed

7 hours ago
  • #retinal degeneration
  • #blue light damage
  • #UFMylation
  • Blue light damage (BLD) is linked to ocular diseases like age-related macular degeneration and dry eye diseases.
  • Photoreceptor cilium disruption is identified as a key event in BLD.
  • UFMylation of kinesin family member 11 (KIF11) decreases under BLD conditions.
  • UFL1, the sole ligase for UFMylation, localizes to the basal body and is essential for maintaining photoreceptor cilia.
  • Blue light exposure disrupts UFL1 localization at the basal body, leading to ciliary defects and photoreceptor dysfunction.
  • Ufl1 knockout mice show similar ciliary defects and retinal impairments.
  • Enhancing UFMylation or ciliogenesis via intravitreal injection can mitigate blue light-induced retinal damage.
  • Targeting the UFMylation-cilium axis is a promising therapeutic strategy for BLD-associated retinal diseases.